[Case of Caroli's disease].

نویسندگان

  • C Pagano
  • M Barberis
  • P Giacchino
  • A Valletti
چکیده

Multiple communicating cysts of the biliary tree, or Caroli's disease (Caroli, 1958), may represent a rare variant of the less uncommon choledochal cyst (Esguerra-Gomez and RiverosGamboa, 1965). Reviewing 500 cases of choledochal cyst, Lee (1969) quotes only one of multiple cysts (Engle and Salmon, 1964). Of three cases similar to the one reported here one presented at the age of 43 with acute cholecystitis (Glenn, 1971); another, aged 31, with recurrent upper abdominal pain (Esguerra-Gomez and Riveros-Gamboa, 1965); and the third, aged 10, with traumatic biliary peritonitis (Engle and Salmon, 1964). In none was the full implications of the diagnosis realized at the first operation and each patient required further surgery. Two are now symptom free with a choledochojejunostomy, and the third has a choledochoduodenostomy.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Caroli's Disease as a Cause of Chronic Epigastric Abdominal Pain: Two Case Reports and a Brief Review of the Literature

Caroli's disease is a very rare congenital malformation, currently included in cystic diseases of the biliary tract, and is characterized by ectasia and dilatation of the intrahepatic bile ducts. Two clinical entities can be distinguished, Caroli's disease in which congenital hepatic impairment is limited to cystic dilatation and Caroli's syndrome in which congenital hepatic fibrosis coexists. ...

متن کامل

Caroli's disease misdiagnosed as intraductal papillary neoplasm of the bile duct

Caroli's disease is a rare autosomal-recessive disorder caused by malformation of the ductal plate during embryonic development. Although it is present at birth, Caroli's disease is typically not diagnosed until between the second and fourth decades of life, as it was in the present patient. Here we report a rare case of Caroli's disease limited to one liver segment, which was initially misdiag...

متن کامل

Epithelial dysplasia in Caroli's disease.

We report a young patient with a solitary intrahepatic cyst without demonstrable connection with the biliary tree. The operative appearances suggested hydatid disease but histological examination of the resected cyst showed that it was the result of Caroli's disease already complicated by severe dysplasia. This case provides further evidence for the premalignant nature of Caroli's disease.

متن کامل

Adenocarcinoma in Caroli's Disease Treated by Liver Transplantation

Caroli's disease is characterized by congenital cystic dilatation of the intrahepatic bile ducts. In 7% of cases a malignant tumor develops complicating the course of the disease. We report the case of a 25 year-old woman in whom Caroli's disease was diagnosed at the age of 11. From that time on, she had several episodes of cholangitis. In 1989, the abdominal ultrasound and CT scan showed dilat...

متن کامل

Caroli's Syndrome in a Post Renal Transplant Patient: Case Report and Review of the Literature

Caroli's syndrome is characterized by bile duct ectasia in association with hepatic fibrosis. It is usually transmitted in an autosomal recessive fashion and has been well documented to be associated with autosomal recessive polycystic kidney disease and occasionally with autosomal dominant polycystic kidney disease. However, there has been only few case reports published with Caroli's syndrome...

متن کامل

Abernethy malformation associated with Caroli’s syndrome in a patient with a PKHD1 mutation: a case report

BACKGROUND Abernethy malformation is a rare congenital anomaly characterised by the partial or complete absence of the portal vein and the subsequent development of an extrahepatic portosystemic shunt. Caroli's disease is a rare congenital condition characterised by non-obstructive saccular intrahepatic bile duct dilation. Caroli's disease combined with congenital hepatic fibrosis and/or renal ...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:
  • Minerva dietologica e gastroenterologica

دوره 25 1  شماره 

صفحات  -

تاریخ انتشار 1971