[Case of Caroli's disease].
نویسندگان
چکیده
Multiple communicating cysts of the biliary tree, or Caroli's disease (Caroli, 1958), may represent a rare variant of the less uncommon choledochal cyst (Esguerra-Gomez and RiverosGamboa, 1965). Reviewing 500 cases of choledochal cyst, Lee (1969) quotes only one of multiple cysts (Engle and Salmon, 1964). Of three cases similar to the one reported here one presented at the age of 43 with acute cholecystitis (Glenn, 1971); another, aged 31, with recurrent upper abdominal pain (Esguerra-Gomez and Riveros-Gamboa, 1965); and the third, aged 10, with traumatic biliary peritonitis (Engle and Salmon, 1964). In none was the full implications of the diagnosis realized at the first operation and each patient required further surgery. Two are now symptom free with a choledochojejunostomy, and the third has a choledochoduodenostomy.
منابع مشابه
Caroli's Disease as a Cause of Chronic Epigastric Abdominal Pain: Two Case Reports and a Brief Review of the Literature
Caroli's disease is a very rare congenital malformation, currently included in cystic diseases of the biliary tract, and is characterized by ectasia and dilatation of the intrahepatic bile ducts. Two clinical entities can be distinguished, Caroli's disease in which congenital hepatic impairment is limited to cystic dilatation and Caroli's syndrome in which congenital hepatic fibrosis coexists. ...
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We report a young patient with a solitary intrahepatic cyst without demonstrable connection with the biliary tree. The operative appearances suggested hydatid disease but histological examination of the resected cyst showed that it was the result of Caroli's disease already complicated by severe dysplasia. This case provides further evidence for the premalignant nature of Caroli's disease.
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Caroli's syndrome is characterized by bile duct ectasia in association with hepatic fibrosis. It is usually transmitted in an autosomal recessive fashion and has been well documented to be associated with autosomal recessive polycystic kidney disease and occasionally with autosomal dominant polycystic kidney disease. However, there has been only few case reports published with Caroli's syndrome...
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BACKGROUND Abernethy malformation is a rare congenital anomaly characterised by the partial or complete absence of the portal vein and the subsequent development of an extrahepatic portosystemic shunt. Caroli's disease is a rare congenital condition characterised by non-obstructive saccular intrahepatic bile duct dilation. Caroli's disease combined with congenital hepatic fibrosis and/or renal ...
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ورودعنوان ژورنال:
- Minerva dietologica e gastroenterologica
دوره 25 1 شماره
صفحات -
تاریخ انتشار 1971